Pediatr Cardiol 27:381–384, 2006

DOI: 10.1007/s00246-005-1270-3


Enlarged Left Vitelline Vein Remnant as a Cause of Cyanosis after the Fontan Procedure: Resolution with an Amplatzer Vascular Plug



Abraham Rothman, MD, Ruben J Acherman, MD, Carlos F Luna, MD, Humberto Restrepo, MD, MPH



ChildrenŐs Heart Center Nevada, 3006 S Maryland Pkwy, Suite 690, Las Vegas, NV 89109, USA.




A 6-year-old girl with heterotaxy and a functional single ventricle had persistent cyanosis 4 years after a fenestrated Fontan procedure. Cardiac catheterization revealed a large venous fistula from a left-sided hepatic vein to the coronary sinus, resulting in desaturation. The anomalous vein was occluded with an Amplatzer vascular plug.


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