Congenital Heart Disease.
2017 Sep; 12(5):583-587
DOI 10.1111/chd.12487
Received: 25 April 2017 /
Accepted: 11 May 2017
Epub 2017 Jun 5
© 2017 Wiley Periodicals,
Inc.
Right aortic arch with situs solitus frequently heralds a
vascular ring
Author
William N Evans,
MD, Ruben J Acherman, MD, Michael L Ciccolo, MD, Sergio A Carrillo, MD, Gary A
Mayman, MD, Carlos f Luna, MD, Robert C Rollins, MD, William J Castillo, MD, Alvaro
Galindo, MD, Abraham Rothman, MD, John A Alexander,
MD, Tina W Kwan, MD, Humberto Restrepo, MD, MPH
Source
Children’s Heart
Center Nevada, 3006 S Maryland Pkwy, Ste 690, Las Vegas, Nevada 89109, USA. Email:
wnevans50@aol.com.
Abstract
Objective: We hypothesized that a right aortic
arch in situs solitus, with or without an associated cardiovascular
malformation, is often associated with a vascular ring.
Methods: From those born in Southern Nevada
between March 2012 and March 2017, we identified 50 (3.6 per 10,000 live
births) with a right aortic arch and situs solitus. From the 50 patients, 6 did
not meet inclusion criteria for further analysis.
Results: Of the 44 remaining, 33 (75%) had a
vascular ring. Of the 33 with a vascular ring, 26 (79%) occurred with an
isolated right aortic arch, and 7 (21%) had an associated cardiovascular malformation.
Of the total 44 patients with a right aortic arch in situs solitus, 34 (79%)
were diagnosed prenatally.
Conclusions: In conclusion, we found a right aortic
arch in situs solitus was often associated with a vascular ring. Further, to
the best of our knowledge, no previous general population study has demonstrated
an equal or higher right aortic arch, prenatal detection rate of 79%.