Progress in Pediatric
Cardiology
Volume 53, June
2019, Pages 42-46
© 2018 Elsevier B.V.
doi:10.1016/j.ppedcard.2018.10.006
Received 27 August 2018,
Revised 29 October 2018, Accepted 30 October 2018, Available online 15 January
2019
Vascular rings and slings:
Contemporary observations.
Authors
William N Evans,
MD, Ruben J Acherman, MD, Michael L Ciccolo, MD, Dean Berthoty, MD,
Gary A Mayman, MD, Humberto Restrepo, MD, MPH
Source
Children’s Heart
Center Nevada, 3006 S Maryland Pkwy, Ste 690, Las Vegas, NV 89109, USA.
Email: wnevans50@aol.com.
Abstract
We reviewed our
recent experience with vascular
rings and slings, including observations from diagnostic imaging and
surgery. We analyzed data from all patients diagnosed with a vascular ring or
sling between September 2015 and August 2018. Our definition of vascular rings
or slings did not include a left aortic
arch with an aberrant right
subclavian artery, accompanied by a left ductus
arteriosus or ligamentum. We identified 74 patients for analysis. Of
the 74, 45 (61%) had a right aortic arch with aberrant left
subclavian artery and left-sided ductus arteriosus or ligamentum, 14
(19%) had a right aortic arch with a left-sided ductus or ligamentum and a
normal left subclavian artery, 11 (15%) had a double
aortic arch, 2 (3%) had a pulmonary
artery sling, and 2 (3%) had a left aortic arch with aberrant right
subclavian artery and a right-sided ductus arteriosus or ligamentum. Of the 74
patients, 40 (54%) were born in Nevada between January 2017 and August 2018. Of
these 40, 33 (83%) were diagnosed prenatally. For the period January 2017 to
August 2018, there were approximately 54,000 live births in Nevada. For right
aortic arch versus double aortic vascular rings, 31 had a right aortic arch
vascular ring for a prevalence of 5.7 per 10,000 live births, and 6 had a
double aortic arch vascular ring for a prevalence of 1.1 per 10,000 live births
(p = 0.0001). Vascular rings are common congenital cardiovascular
malformations, especially right aortic arch vascular rings. Further, a high
percentage of vascular rings can be detected prenatally.