Prenatal Diagnosis 2019;39:1220–1224.
DOI: 10.1177/2045894019876545
Date received: 11 July 2019; Revised: 10 September 2019; Accepted: 19 September 2019
ã 2019 John Wiley & Sons, Ltd.
Persistent right umbilical vein in isomerism
Author
Ruben J. Acherman, MD, William N. Evans, MD
Source
William N. Evans,
Children's Heart Center
Nevada, 3006 S.
Maryland Pkwy, Ste. 690, Las
Vegas, NV 89109.
Email: wnevans50@aol.com
Abstract
Objective: Our
objective was to evaluate the incidence of a persistent right umbilical vein in
isomerism versus situs solitus.
Methods: For this
retrospective, observational, nonrandomized report, we identified fetuses with
confirmed right umbilical veins from all patients referred for fetal
echocardiography
in Southern Nevada between January 2006 and January 2019.
Results: For the
period January 2006 to January 2019, we identified 89 fetuses with situs solitus and a right umbilical vein from 16 320 women
undergoing prenatal
cardiac
evaluation, resulting in a right umbilical vein incidence of 0.5% in situs solitus. For the same period, we identified 36 fetuses with
isomerism and confirmatory
umbilical vein
imaging. Of the 36, 15 (42%) had right umbilical veins. Of the15, four of 11
(19%) had left isomerism, and 11 of 15 (73%) had right isomerism(P
= .006).
Conclusions: A
right umbilical vein is rare with situs solitus and
common with isomerism. A right umbilical vein is more common in right isomerism
than left isomerism
and should alert
the clinician to check for isomeric situs, especially right isomerism.