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J Arrhythmia. 2019;35:494498.

DOI: 10.1002/joa3.12193

Received: 12 January 2019 / Accepted: 19 April 2019

 

Permanent junctional reciprocating tachycardia in infants and children

 

Authors

Ranjit I Kylat, MD, Ricardo A Samson, MD

 

Source

Ranjit I. Kylat, Division of Neonatal-Perinatal Medicine and Developmental Biology, Department of Pediatrics, University of Arizona, College of Medicine, PO BOX 245073, 1501 N Campbell Avenue, Tucson, AZ 85724. Email: rkylat@gmail.com

 

Abstract

Permanent junctional reciprocating tachycardia (PJRT) is a rare form of supraventricular tachycardia (SVT). It generally presents in infants but can be difficult to diagnose. The characteristic EKG findings, response to Adenosine and persistence or frequent recurrences are helpful in making the diagnosis. It is usually difficult to manage with the initial and single medications used in SVT. Many patients are misdiagnosed and not treated effectively and end up having end stage cardiomyopathy and are diagnosed in patients referred for transplant. Hence all patients referred for a cardiac transplant with dilated cardiomyopathy need to be evaluated for this arrhythmia. If appropriate treatment is started early in the course, the failure can be ameliorated, and the cardiomyopathy can be resolved.

 

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